四川大學(xué)華西醫(yī)院ALS研究匯報(bào)【精品-】

1、橫斷面調(diào)查報(bào)告2008年ALS研究、臨床、教學(xué)、患者教育等情況研究：主要是臨床研究臨床：開設(shè)了專病門診教學(xué)：病房收治病人，為醫(yī)學(xué)生的見習(xí)提供學(xué)習(xí)機(jī)會患者教育：我們對所有收治過的ALS病人進(jìn)行隨訪2008年ALS學(xué)術(shù)成果（含壁報(bào)）國家自然科學(xué)基金一項(xiàng)：一個(gè)遠(yuǎn)端型脊肌萎縮癥家系的基因定位研究國際會議壁報(bào)兩篇：1）Clinical and genetic features of patients with amyotrophic lateral sclerosis in South-West China2）Clinical and genetic analysis of a large Chines

2、e family with amyotrophic lateral sclerosis 2009年ALS工作計(jì)劃和目標(biāo)神經(jīng)內(nèi)科住院病房成立ALS疾病組；加強(qiáng)ALS?？崎T診的建設(shè)；為四川地區(qū)的病人進(jìn)行一次該病教育會；爭取發(fā)表高質(zhì)量的文章；進(jìn)行ALS的臨床和基礎(chǔ)研究和申報(bào)課題。Accept:Clinical and genetic features of sporadic patients with amyotrophic lateral sclerosis in southwest China. Amyotrophic Lateral Sclerosis. 2009, (1-6).Structu

3、ral and Functional Changes Mapped in the Brains of Amyotrophic Lateral Sclerosis patients with/without dysphagia: A pilot study. MALS-2009-0019.R2Clinical Features of Hirayama Disease in mainland China. MALS-2009-0044Published:文章The mean age of onset was 50.911.4 years (range 24.275.9 years).Thirty-

4、five patients (21.7%) were younger than 40 years of age.The mean delay between onset age and age at diagnosis was 16.514.3 months. The mean disease duration was 30.723.5 months.Forty patients (24.8%) died during follow-up from respiratory failure or bulbar paralysis. The mean survival time after ons

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